![]() ![]() If the airway is extremely compromised, bilateral mandibular osteotomies with distraction osteogenesis may be performed. The first step to correction is dependent on the patient’s airway stability. The benefit of this less intrusive procedure is no visible facial scars. This adhesion is released at a later date after the goals of improved feeding and growth have allowed the airway to enlarge. Sometimes a tongue lip adhesion may be performed, sewing the posteriorly displaced tongue forward to the inside of the lower lip opening the airway. In more mild cases, the neonate may be placed in a prone position, or a nasopharyngeal tube may be inserted through the nose to maintain airway patency. If left untreated, patients have problems with feeding, obstructive sleep apnea, ear infections, and reduced hearing. Initially, when airway obstruction occurs, the primary goal is to create an adequate airway by using distractor techniques that prevent the need for a tracheostomy. Those children born with a cleft palate should be seen by an Ear, Nose and Throat (ENT) specialist who will carefully monitor fluid buildup behind the ear. The causes of Pierre Robin Syndrome are unknown however, Robin sequence is seen in a number of genetic syndromes. As a result of the physical characteristics of Pierre Robin Syndrome, both feeding and breathing difficulties are often present in varying degrees of severity. Often there is an associated cleft of the soft palate resulting from the posteriorly displaced tongue interfering with normal palate development in utero. Pierre Robin Syndrome is characterized by the triad, or sequence of findings: micrognathia (small lower jaw), glossoptosis (the tongue tends to fall back and downwards), and airway compromise. ![]()
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